{"id":"7a1b0cd3-e0f8-4211-996e-3fce949c31ff","slug":"spinal-intradural-solitary-fibrous-tumor-hemangiopericytoma-with-intramedullary-invasion-mimicking-a-hemangioblastoma","title":"Spinal intradural solitary fibrous tumor/ hemangiopericytoma with intramedullary invasion mimicking a hemangioblastoma","authors":["Shanta Thapa","Hitoshi Yamahata","Tomohisa Okada","Masanori Yonenaga","Madan Bajagain","Ryutaro Makino","Ryosuke Hanaya"],"abstract":"Background: Solitary fibrous tumor/hemangiopericytomas (SFT/HPCs) are rare mesenchymal tumors of nonmeningothelial origin that comprises <1% of all central nervous system tumors. Case Description: A 45-year-old male presented with sleep apnea (apnea-hypopnea index was 17.1 events/hour) and dysesthesias of the right upper and lower extremities. The magnetic resonance demonstrated a heterogeneous intradural extra-axial C1 mass with syringobulbia and syringomyelia. The right vertebral angiography revealed a hypervascular mass (i.e., intense tumor staining). With the preoperative diagnosis of a spinal hemangioblastoma, the patient underwent tumor removal. However, intraoperative findings demonstrated that the ventral component of the tumor was intramedullary without a dural attachment. Further, the histological diagnosis was consistent with SFT/HPC (HPC phenotype). The postoperative course was uneventful, and the patient’s symptoms and the syrinxes spontaneously regressed. Conclusion: A 45-year-old male presented a rare spinal intradural lesion at C1 appeared to be a spinal hemangioblastoma, but proved to be SFT/HPC (HPC phenotype) with intramedullary invasion.","thumbnailUrl":"https://sni-digital-videos.s3.amazonaws.com/articles/7a1b0cd3-e0f8-4211-996e-3fce949c31ff/featured/hero-1781560895620.png","publishDate":"2022-09-30T00:00:00.000Z","doi":"10.25259/SNI_655_2022","categories":["Spine","Case Report"],"fullTextUrl":"https://surgicalneurologyint.com/wp-content/uploads/2022/09/11907/SNI-13-443.pdf"}