{"id":"12c4e499-cd8f-42e5-be53-dc02b1245f15","slug":"spontaneous-spinal-epidural-hematoma-in-a-pediatric-hemophiliac","title":"Spontaneous spinal epidural hematoma in a pediatric hemophiliac","authors":["Gianluca Scalia","Massimiliano Porzio","Roberta Costanzo","Domenico Gerardo Iacopino","Gianluca Galvano","Giovanni Federico Nicoletti","Giuseppe Emmanuele Umana"],"abstract":"Background: Spontaneous spinal epidural hematomas (SSEH), unrelated to trauma, epidural anesthesia, or surgery, are rare in the pediatric population. Here, a 1-year-old male with hemophilia presented with a magnetic resonance (MR)-documented SSEH and was successfully treated with a C5-T10 right hemilaminectomy. Case Description: A 1-year-old male with hemophilia presented with quadriparesis. The holo-spine magnetic resonance imaging with contrast showed a posterior cervicothoracic compressive epidural lesion extending from C3 to L1 consistent with an epidural hematoma. He underwent a C5 to T10 right-sided hemilaminectomy for clot removal, following which his motor deficits fully resolved. A literature review of SSEH attributed to hemophilia revealed that 28 of 38 cases were effectively treated conservatively, while only 10 cases warranted surgical decompression. Conclusion: Select patients with SSEH attributed to hemophilia with severe MR-documented cord/cauda equina compromise and significant accompanying neurological deficits may require emergent surgical decompression.","thumbnailUrl":"https://sni-digital-videos.s3.amazonaws.com/articles/12c4e499-cd8f-42e5-be53-dc02b1245f15/featured/hero-1781560493936.png","publishDate":"2023-02-24T00:00:00.000Z","doi":"10.25259/SNI_82_2023","categories":["Spine","Case Report"],"fullTextUrl":"https://surgicalneurologyint.com/api/articles/12c4e499-cd8f-42e5-be53-dc02b1245f15/pdf"}